{"id":16611,"date":"2023-03-15T10:12:02","date_gmt":"2023-03-15T14:12:02","guid":{"rendered":"https:\/\/www.progeriaresearch.org\/?p=16611"},"modified":"2025-02-15T17:46:23","modified_gmt":"2025-02-15T22:46:23","slug":"progerinbiomarker","status":"publish","type":"post","link":"https:\/\/www.progeriaresearch.org\/id\/2023\/03\/15\/progerinbiomarker\/","title":{"rendered":"Tonggak-tonggak penelitian yang menarik dalam evaluasi perawatan dan perpanjangan hidup!"},"content":{"rendered":"<p>[et_pb_section fb_built=\u201d1\u2033 _builder_version=\u201d4.16\u2033 custom_padding=\u201d0px|||||\u201d global_colors_info=\u201d{}\u201d][et_pb_row _builder_version=\u201d4.16\u2033 background_size=\u201dinitial\u201d background_position=\u201dtop_left\u201d background_repeat=\u201drepeat\u201d custom_padding=\u201d||5px|||\u201d global_colors_info=\u201d{}\u201d][et_pb_column type=\u201d4_4\u2033 _builder_version=\u201d4.16\u2033 custom_padding=\u201d|||\u201d global_colors_info=\u201d{}\u201d custom_padding__hover=\u201d|||\u201d][et_pb_text _builder_version=\u201d4.24.0\u2033 background_size=\u201dinitial\u201d background_position=\u201dtop_left\u201d background_repeat=\u201drepeat\u201d global_colors_info=\u201d{}\u201d]<\/p>\n<h5>Kami sangat gembira untuk berbagi dua pembaruan penelitian yang menarik dengan Anda, yang diterbitkan secara online hari ini di jurnal kardiovaskular terkemuka di dunia, <em>Sirkulasi <a href=\"https:\/\/www.progeriaresearch.org\/id\/progerinbiomarker\/#1\">(1)<\/a><\/em>:<\/h5>\n<p>&nbsp;<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"wp-image-16615 aligncenter\" src=\"https:\/\/www.progeriaresearch.org\/wp-content\/uploads\/2023\/03\/27-year-old-Sammy-from-Italy-shows-how-much-he-loves-this-exciting-research-news.png\" alt=\"\" width=\"415\" height=\"355\" \/><\/p>\n<p><span style=\"color: #ff0000;\"><strong><u>Biomarker pada Progeria<\/u><\/strong><\/span><\/p>\n<p>Sebuah cara baru untuk mengukur progerin, protein toksik yang menyebabkan Progeria, telah dikembangkan oleh tim yang dipimpin oleh salah satu pendiri PRF dan Direktur Medis, Dr. Leslie Gordon. Dengan ditemukannya biomarker ini, yang menggunakan plasma darah untuk mengukur kadar progerin, <strong>Para peneliti dapat memahami bagaimana pengobatan mempengaruhi peserta uji klinis setelah periode waktu yang lebih singkat<\/strong> dan di beberapa titik sepanjang setiap uji klinis.<\/p>\n<p>Pengujian ini dapat mengoptimalkan proses uji klinis dengan <strong>menyediakan informasi awal tentang efektivitas perawatan yang sedang diuji<\/strong>, sebagai pendahuluan untuk uji klinis lain seperti penambahan berat badan, perubahan dermatologis, kontraktur dan fungsi sendi, dll., yang semuanya memerlukan waktu lebih lama untuk terwujud. Fitur klinis Progeria ini merupakan ukuran efek pengobatan jangka panjang yang penting yang kini dilengkapi dengan kadar progerin yang diukur lebih awal dalam terapi. Kita kini mungkin dapat memahami manfaat pengobatan sedini empat bulan setelah memulai pengobatan, atau menghentikan pengobatan yang mungkin tidak bermanfaat bagi peserta uji coba, untuk menghindari efek samping yang tidak perlu.<\/p>\n<p><strong><span style=\"color: #ff0000;\"><u>Hidup lebih lama dengan lonafarnib<\/u><\/span><\/strong><\/p>\n<p>Selain mempercepat penemuan pengobatan dan penyembuhan di masa depan, cara baru dan inovatif untuk mengukur progerin ini menunjukkan bahwa <strong>manfaat jangka panjang lonafarnib untuk anak-anak dengan Progeria lebih besar dari yang ditentukan sebelumnya<\/strong>.<\/p>\n<p>Data penelitian menunjukkan bahwa kadar progerin yang lebih rendah dalam darah mencerminkan manfaat kelangsungan hidup: semakin lama seseorang dengan Progeria menjalani lonafarnib, semakin besar manfaat kelangsungan hidup dari menjalani terapi. Kadar progerin menurun sekitar 30-60% selama obat tersebut dikonsumsi, dan harapan hidup pasien yang menjalani pengobatan selama lebih dari 10 tahun meningkat rata-rata 4,5 tahun. <strong>peningkatan lebih dari 30% dalam harapan hidup rata-rata, dari 14,5 tahun menjadi hampir 20 tahun<\/strong>!<\/p>\n<p>[\/et_pb_text][\/et_pb_column][\/et_pb_row][et_pb_row _builder_version=\u201d4.16\u2033 background_size=\u201dinitial\u201d background_position=\u201dtop_left\u201d background_repeat=\u201drepeat\u201d global_colors_info=\u201d{}\u201d][et_pb_column type=\u201d4_4\u2033 _builder_version=\u201d4.16\u2033 custom_padding=\u201d|||\u201d global_colors_info=\u201d{}\u201d custom_padding__hover=\u201d|||\u201d][et_pb_button button_url=\u201dhttps:\/\/www.progeriaresearch.org\/wp-content\/uploads\/2023\/03\/Progerin-Plasma-Biomarker-press-release-FINAL.pdf\u201d button_text=\u201dUntuk mempelajari lebih lanjut, lihat siaran pers kami di sini\u201d button_alignment=\u201dcenter\u201d admin_label=\u201dbiomarker pdf\u201d _builder_version=\u201d4.19.5\u2033 _module_preset=\u201ddefault\u201d button_text_color=\u201d#FFFFFF\u201d button_bg_color=\u201d#00B2E2\u2033 button_border_width=\u201d0px\u201d button_border_color=\u201d#00B2E2\u2033 background_layout=\u201ddark\u201d] global_colors_info=\u201d{}\u201d][\/et_pb_button][et_pb_text _builder_version=\u201d4.19.5\u2033 _module_preset=\u201ddefault\u201d global_colors_info=\u201d{}\u201d]<\/p>\n<p style=\"font-weight: 400;\"><strong>\u201cSalah satu kisah paling luar biasa yang pernah dibagikan di podcast ini\u201d<br \/><\/strong>\u2013 Dr. Carolyn Lam, spesialis jantung terkenal di dunia dan pembawa acara podcast <em>Sirkulasi dalam Pelarian, <\/em>dalam perjalanan yang menghasilkan temuan menarik ini<em>. <\/em><strong>Dengarkan wawancara selengkapnya<\/strong> tentang dampak mendalam dari penelitian ini langsung dari Dr. Gordon. Dengarkan <a href=\"https:\/\/r20.rs6.net\/tn.jsp?f=001cLXauJ5R6hFjgU6UNVj8z1ubk-cU5xChRkxoAUyz5uADnaWoiVSXmGDO6nDbCFI6BusWzoswFG0iru8PXvTinayQ2nuBWZkmbHn8pNOQ-qsUB1VpMUndro-VBH-aWDvJUzVgfNvTim0xjz6cUlYUsEKvW6Ac2WVwzATNn1BxwmDhQLC1rKekmK7seL8r8YfP&amp;c=WFQd6JESprJMCu4rKF2oA9DZh92aflFfVggkN5fMTdEL4z9YqYGm8g==&amp;ch=BuG-LaRM92CDJVKzSsfwhIYuKm0CXdEFhP1J1G8vN4oKaWQGcoaRLw==\"><strong>Di Sini<\/strong><\/a> <a href=\"https:\/\/r20.rs6.net\/tn.jsp?f=001cLXauJ5R6hFjgU6UNVj8z1ubk-cU5xChRkxoAUyz5uADnaWoiVSXmGDO6nDbCFI6BusWzoswFG0iru8PXvTinayQ2nuBWZkmbHn8pNOQ-qsUB1VpMUndro-VBH-aWDvJUzVgfNvTim0xjz6cUlYUsEKvW6Ac2WVwzATNn1BxwmDhQLC1rKekmK7seL8r8YfP&amp;c=WFQd6JESprJMCu4rKF2oA9DZh92aflFfVggkN5fMTdEL4z9YqYGm8g==&amp;ch=BuG-LaRM92CDJVKzSsfwhIYuKm0CXdEFhP1J1G8vN4oKaWQGcoaRLw==\">(<\/a>mulai pada 6:41).<\/p>\n<p>[\/et_pb_text][et_pb_button button_url=\u201dhttps:\/\/circulation.libsyn.com\/circulation-june-6-2023-issue\u201d button_text=\u201dDengarkan Dr. Leslie Gordon di podcast Circulation on the Run\u201d button_alignment=\u201dcenter\u201d admin_label=\u201dcirculation podcast\u201d _builder_version=\u201d4.19.5\u2033 _module_preset=\u201ddefault\u201d button_text_color=\u201d#FFFFFF\u201d button_bg_color=\u201d#00B2E2\u2033 button_border_width=\u201d0px\u201d button_border_color=\u201d#00B2E2\u2033 background_layout=\u201ddark\u201d global_colors_info=\u201d{}\u201d][\/et_pb_button][et_pb_text _builder_version=\u201d4.19.5\u2033 _module_preset=\u201ddefault\u201d global_colors_info=\u201d{}\u201d]<\/p>\n<p style=\"font-weight: 400;\">Dan pada bulan Juni, dua makalah editorial <a href=\"https:\/\/www.progeriaresearch.org\/id\/progerinbiomarker\/#2\">(2) <\/a>Dan <a href=\"https:\/\/www.progeriaresearch.org\/id\/progerinbiomarker\/#3\">(3)<\/a> dipublikasikan di <i>Sirkulasi <\/i>menyoroti pentingnya biomarker ini untuk memajukan perawatan dan penyembuhan bagi anak-anak penderita Progeria dan untuk lebih memahami penuaan.<\/p>\n<p>[\/et_pb_text][et_pb_text admin_label=\u201dpapers\u201d module_id=\u201d1\u2033 _builder_version=\u201d4.19.5\u2033 background_size=\u201dinitial\u201d background_position=\u201dtop_left\u201d background_repeat=\u201drepeat\u201d global_colors_info=\u201d{}\u201d]<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"wp-image-16634 alignleft\" src=\"https:\/\/www.progeriaresearch.org\/wp-content\/uploads\/2023\/03\/Circulation-logo-300x74.jpg\" alt=\"\" width=\"219\" height=\"54\" srcset=\"https:\/\/www.progeriaresearch.org\/wp-content\/uploads\/2023\/03\/Circulation-logo-300x74.jpg 300w, https:\/\/www.progeriaresearch.org\/wp-content\/uploads\/2023\/03\/Circulation-logo.jpg 400w\" sizes=\"(max-width: 219px) 100vw, 219px\" \/><\/p>\n<p>&nbsp;<\/p>\n<hr \/>\n<p>(1) Gordon, LB, Norris, W., Hamren, S., <em>dan lain-lain<\/em>Plasma Progerin pada Pasien dengan Sindrom Progeria Hutchinson-Gilford: Pengembangan Imunoassay dan Evaluasi Klinis. <em>Sirkulasi<\/em>, 2023<\/p>\n<p>(2) <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/37276254\/\">Perkembangan Kelainan Jantung pada Sindrom Progeria Hutchinson-Gilford: Sebuah Studi Longitudinal Prospektif.<\/a><br \/>Olsen FJ, Gordon LB, Smoot L, Kleinman ME, Gerhard-Herman M, Hegde SM, Mukundan S, Mahoney T, Massaro J, Ha S, Prakash A.<br \/><em>Sirkulasi<\/em>. 6 Juni 2023;147(23):1782-1784. doi: 10.1161\/CIRCULATIONAHA.123.064370. Terbit secara elektronik 5 Juni 2023.<\/p>\n<p style=\"font-weight: 400;\">(3) <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/37276251\/\">Alat yang Tersedia untuk Mendeteksi Progerin dan Perkembangan Penyakit Jantung pada Sindrom Progeria Hutchinson-Gilford. <\/a><br \/>Eriksson M, Haugaa K, Rev\u00eachon G.<br \/><em>Sirkulasi<\/em>. 6 Juni 2023;147(23):1745-1747. doi: 10.1161\/CIRCULATIONAHA.123.064765. Terbit secara elektronik 5 Juni 2023.<\/p>\n<p>[\/et_pb_teks][\/et_pb_kolom][\/et_pb_baris][\/et_pb_bagian]<\/p>","protected":false},"excerpt":{"rendered":"<p>Tim peneliti kami telah menemukan cara baru yang penting untuk mengukur progerin, protein beracun yang menyebabkan Progeria. Dengan penemuan ini, para ilmuwan juga menemukan bahwa manfaat jangka panjang lonafarnib bagi anak-anak penderita Progeria lebih besar dari yang kita duga.<br \/>\nApa arti kedua temuan ini bagi komunitas Progeria? <\/p>","protected":false},"author":2,"featured_media":16614,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_et_pb_use_builder":"on","_et_pb_old_content":"","_et_gb_content_width":"","footnotes":"","_links_to":"","_links_to_target":""},"categories":[2,1],"tags":[],"class_list":["post-16611","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-news","category-uncategorized"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.8 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Progerin Biomarker | The Progeria Research Foundation<\/title>\n<meta name=\"description\" content=\"Our research team has discovered a vital new way to measure progerin, the toxic protein that causes Progeria. With this discovery, scientists also found that the long-term benefit of lonafarnib for children with Progeria is greater than we thought. What do these two findings mean for the Progeria community? Read more here\u2026\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.progeriaresearch.org\/id\/2023\/03\/15\/progerinbiomarker\/\" \/>\n<meta property=\"og:locale\" content=\"id_ID\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Progerin Biomarker | The Progeria Research Foundation\" \/>\n<meta property=\"og:description\" content=\"Our research team has discovered a vital new way to measure progerin, the toxic protein that causes Progeria. With this discovery, scientists also found that the long-term benefit of lonafarnib for children with Progeria is greater than we thought. 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Read more here\u2026\" \/>\n<meta property=\"og:url\" content=\"https:\/\/www.progeriaresearch.org\/id\/2023\/03\/15\/progerinbiomarker\/\" \/>\n<meta property=\"og:site_name\" content=\"The Progeria Research Foundation\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/ProgeriaResearch\/\" \/>\n<meta property=\"article:published_time\" content=\"2023-03-15T14:12:02+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2025-02-15T22:46:23+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/www.progeriaresearch.org\/wp-content\/uploads\/2023\/03\/Sammy-7.jpg\" \/>\n\t<meta property=\"og:image:width\" content=\"640\" \/>\n\t<meta property=\"og:image:height\" content=\"480\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"author\" content=\"Karen Betournay\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:creator\" content=\"@Progeria\" \/>\n<meta name=\"twitter:site\" content=\"@Progeria\" \/>\n<meta name=\"twitter:label1\" content=\"Written by\" \/>\n\t<meta name=\"twitter:data1\" content=\"Karen Betournay\" \/>\n\t<meta name=\"twitter:label2\" content=\"Est. reading time\" \/>\n\t<meta name=\"twitter:data2\" content=\"3 menit\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\/\/www.progeriaresearch.org\/2023\/03\/15\/progerinbiomarker\/#article\",\"isPartOf\":{\"@id\":\"https:\/\/www.progeriaresearch.org\/2023\/03\/15\/progerinbiomarker\/\"},\"author\":{\"name\":\"Karen Betournay\",\"@id\":\"https:\/\/www.progeriaresearch.org\/ta\/#\/schema\/person\/2be6cec85c11aaef7a7602636c5b9946\"},\"headline\":\"Exciting research milestones in treatment evaluation and life extension!\",\"datePublished\":\"2023-03-15T14:12:02+00:00\",\"dateModified\":\"2025-02-15T22:46:23+00:00\",\"mainEntityOfPage\":{\"@id\":\"https:\/\/www.progeriaresearch.org\/2023\/03\/15\/progerinbiomarker\/\"},\"wordCount\":795,\"publisher\":{\"@id\":\"https:\/\/www.progeriaresearch.org\/ta\/#organization\"},\"image\":{\"@id\":\"https:\/\/www.progeriaresearch.org\/2023\/03\/15\/progerinbiomarker\/#primaryimage\"},\"thumbnailUrl\":\"https:\/\/www.progeriaresearch.org\/wp-content\/uploads\/2023\/03\/Sammy-7.jpg\",\"articleSection\":[\"News\",\"Uncategorized\"],\"inLanguage\":\"id\"},{\"@type\":\"WebPage\",\"@id\":\"https:\/\/www.progeriaresearch.org\/2023\/03\/15\/progerinbiomarker\/\",\"url\":\"https:\/\/www.progeriaresearch.org\/2023\/03\/15\/progerinbiomarker\/\",\"name\":\"Progerin Biomarker | The Progeria Research Foundation\",\"isPartOf\":{\"@id\":\"https:\/\/www.progeriaresearch.org\/ta\/#website\"},\"primaryImageOfPage\":{\"@id\":\"https:\/\/www.progeriaresearch.org\/2023\/03\/15\/progerinbiomarker\/#primaryimage\"},\"image\":{\"@id\":\"https:\/\/www.progeriaresearch.org\/2023\/03\/15\/progerinbiomarker\/#primaryimage\"},\"thumbnailUrl\":\"https:\/\/www.progeriaresearch.org\/wp-content\/uploads\/2023\/03\/Sammy-7.jpg\",\"datePublished\":\"2023-03-15T14:12:02+00:00\",\"dateModified\":\"2025-02-15T22:46:23+00:00\",\"description\":\"Our research team has discovered a vital new way to measure progerin, the toxic protein that causes Progeria. 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