{"id":1868,"date":"2017-05-09T19:35:04","date_gmt":"2017-05-09T19:35:04","guid":{"rendered":"https:\/\/www.progeriaresearch.org\/?page_id=1868"},"modified":"2023-09-22T10:33:55","modified_gmt":"2023-09-22T14:33:55","slug":"workshop-2016","status":"publish","type":"page","link":"https:\/\/www.progeriaresearch.org\/ur\/workshop-2016\/","title":{"rendered":"\u0648\u0631\u06a9\u0634\u0627\u067e 2016"},"content":{"rendered":"<p><strong>\u0645\u0626\u06cc 2-4\u060c 2016; \u06a9\u06cc\u0645\u0628\u0631\u062c\u060c \u0627\u06cc\u0645 \u0627\u06d2<\/strong><\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignright\" src=\"https:\/\/www.progeriaresearch.org\/assets\/images\/medical_images\/ACROSS_AROUND_Nihal-(2).jpg\" width=\"125\" height=\"126\" \/><img loading=\"lazy\" decoding=\"async\" class=\"alignright\" src=\"https:\/\/www.progeriaresearch.org\/assets\/images\/ACROSS_AROUND_Carly.jpg\" width=\"125\" height=\"126\" \/><img loading=\"lazy\" decoding=\"async\" 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\u0627\u0644\u0627\u0626\u0646\u0645\u0646\u0679 \u0645\u0627\u0633 \u0633\u067e\u06cc\u06a9\u0679\u0631\u0648 \u0645\u06cc\u0679\u0631\u06cc (FEA-MS) \u06a9\u06d2 \u0630\u0631\u06cc\u0639\u06d2 \u0645\u0642\u062f\u0627\u0631<\/li>\n<li>\u06c1\u0686\u0646\u0633\u0646-\u06af\u0644\u0641\u0648\u0631\u0688 \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0633\u0646\u0688\u0631\u0648\u0645 \u0645\u06cc\u06ba \u0627\u0648\u0633\u0679\u06cc\u0648\u062c\u06cc\u0646\u06a9 \u062a\u0641\u0631\u06cc\u0642 \u0627\u0648\u0631 \u06c1\u0688\u06cc\u0648\u06ba \u06a9\u06d2 \u0645\u0639\u06cc\u0627\u0631 \u06a9\u06d2 \u062f\u0648\u0631\u0627\u0646 \u06a9\u06cc\u0646\u0646\u06cc\u06a9\u0644 Wnt-\u03b2-catein \u0633\u06af\u0646\u0644\u0646\u06af \u067e\u0627\u062a\u06be \u0648\u06d2 \u06a9\u06d2 \u06a9\u0631\u062f\u0627\u0631 \u06a9\u06cc \u062a\u062d\u0642\u06cc\u0642\u0627\u062a<\/li>\n<li>Lamin A\/C \u06a9\u06cc \u0627\u06cc\u06a9 \u0646\u0626\u06cc \u0634\u06a9\u0644<\/li>\n<li>Everolimus Laminopathy \u062e\u0644\u06cc\u0627\u062a \u06a9\u06cc \u0641\u06cc\u0646\u0648\u0679\u0627\u0626\u067e \u06a9\u0648 \u0628\u06c1\u062a\u0631 \u0628\u0646\u0627\u062a\u0627 \u06c1\u06d2\u06d4<\/li>\n<li>\u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u06a9\u0644\u06cc\u0646\u06cc\u06a9\u0644 \u0679\u0631\u0627\u0626\u0644\u0632 \u06a9\u0627 \u0627\u0633\u06a9\u06cc\u0645\u0627 \u0627\u0648\u0631 \u062c\u0627\u0626\u0632\u06c1<\/li>\n<li>\u039435 \u0627\u0648\u0631 \u039450 \u06a9\u0648 \u062d\u0630\u0641 \u06a9\u0631\u0646\u06d2 \u0633\u06d2 O-GlcNAc \u0645\u06cc\u06ba \u062a\u0631\u0645\u06cc\u0645 \u0634\u062f\u06c1 &#039;\u0633\u0648\u06cc\u0679 \u0633\u067e\u0627\u0679&#039; \u0644\u0627\u0645\u06cc\u0646 \u0627\u06d2 \u0679\u06cc\u0644 \u06a9\u06d2 \u0644\u06cc\u06d2 \u0645\u0646\u0641\u0631\u062f: \u0644\u0627\u0645\u06cc\u0646 \u0627\u06d2 \u06a9\u06d2 \u0645\u06cc\u0679\u0627\u0628\u0648\u0644\u06a9 (\u0688\u0633) \u0631\u06cc\u06af\u0648\u0644\u06cc\u0634\u0646 \u06a9\u06d2 \u0644\u06cc\u06d2 \u0645\u0636\u0645\u0631\u0627\u062a<\/li>\n<li>Exome \u062a\u0633\u0644\u0633\u0644 \u06a9\u06d2 \u0630\u0631\u06cc\u0639\u06d2 Atypical Progeria \u0645\u06cc\u06ba Causative Mutations \u06a9\u06cc \u0646\u0634\u0627\u0646\u062f\u06c1\u06cc \u06a9\u0631\u0646\u0627<\/li>\n<li>\u0645\u06cc\u0679\u0631\u06a9\u0633 \u0645\u06cc\u06ba \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0646 \u06a9\u06cc \u0645\u0642\u062f\u0627\u0631 \u06a9\u06d2 \u0644\u06cc\u06d2 \u0627\u0644\u0679\u0631\u0627 \u0633\u06cc\u0646\u0633\u06cc\u0679\u06cc\u0648 \u0627\u0645\u06cc\u0648\u0646\u0648\u0633\u06d2 \u06a9\u06cc \u062a\u0631\u0642\u06cc<\/li>\n<li>\u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0645\u06cc\u06ba \u0627\u06cc\u062a\u06be\u0631\u0648\u0633\u06a9\u0644\u0631\u0648\u0633\u06cc\u0633: \u06c1\u0631 \u062c\u06af\u06c1 \u0627\u0648\u0631 VSMC \u0645\u062e\u0635\u0648\u0635 \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0646 \u0627\u0638\u06c1\u0627\u0631 \u06a9\u06d2 \u0633\u0627\u062a\u06be \u0646\u0626\u06d2 \u0645\u0627\u0624\u0633 \u0645\u0627\u0688\u0644\u0632 \u0633\u06d2 \u0628\u0635\u06cc\u0631\u062a<\/li>\n<li>\u0627\u0646\u0633\u0627\u0646\u06cc ZMPSTE24 \u0627\u0648\u0631 \u0628\u06cc\u0645\u0627\u0631\u06cc \u06a9\u06d2 \u062a\u063a\u06cc\u0631\u0627\u062a \u06a9\u06cc \u067e\u0631\u0648\u0679\u0648\u0644\u0648\u0679\u06a9 \u0633\u0631\u06af\u0631\u0645\u06cc \u06a9\u0648 \u0648\u0627\u0636\u062d \u06a9\u0631\u0646\u0627<\/li>\n<li>\u06c1\u0686\u0646\u0633\u0646-\u06af\u0644\u0641\u0648\u0631\u0688 \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0633\u0646\u0688\u0631\u0648\u0645 \u06a9\u06d2 \u0639\u0644\u0627\u062c \u06a9\u06d2 \u0644\u06cc\u06d2 JH4 \u0633\u06d2 \u0645\u0627\u062e\u0648\u0630 \u06a9\u06cc\u0645\u06cc\u06a9\u0644\u0632 \u06a9\u0627 \u067e\u0631\u06cc \u06a9\u0644\u06cc\u0646\u06cc\u06a9\u0644 \u062a\u062c\u0632\u06cc\u06c1<\/li>\n<li>\u0648\u0679\u0627\u0645\u0646 \u0688\u06cc \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0646 \u0627\u0638\u06c1\u0627\u0631 \u06a9\u0648 \u06a9\u0645 \u06a9\u0631\u062a\u0627 \u06c1\u06d2 \u0627\u0648\u0631 HGPS \u0633\u06cc\u0644\u0648\u0644\u0631 \u0646\u0642\u0627\u0626\u0635 \u06a9\u0648 \u0628\u06c1\u062a\u0631 \u0628\u0646\u0627\u062a\u0627 \u06c1\u06d2\u06d4<\/li>\n<li>\u0642\u0628\u0644 \u0627\u0632 \u0648\u0642\u062a \u0628\u0691\u06be\u0627\u067e\u06d2 \u0645\u06cc\u06ba \u0627\u06cc\u0646\u0679\u06cc \u0622\u06a9\u0633\u06cc\u0688\u06cc\u0646\u0679 NRF2 \u0631\u0627\u0633\u062a\u06d2 \u06a9\u0627 \u062c\u0628\u0631<\/li>\n<li>\u0627\u0633\u0641\u0646\u06af\u0648\u0644\u067e\u06cc\u0688 \u0645\u06cc\u0679\u0627\u0628\u0648\u0644\u0627\u0626\u0679\u0633 \u0627\u0648\u0631 \u0627\u06cc\u0686 \u062c\u06cc \u067e\u06cc \u0627\u06cc\u0633 \u0641\u06cc\u0646\u0648\u0679\u0627\u0626\u067e<\/li>\n<li>\u06c1\u0686\u0646\u0633\u0646-\u06af\u0644\u0641\u0648\u0631\u0688 \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0633\u0646\u0688\u0631\u0648\u0645 \u06a9\u06d2 \u0645\u0631\u06cc\u0636\u0648\u06ba \u0633\u06d2 \u0645\u0627\u062e\u0648\u0630 \u0641\u0627\u0626\u0628\u0631\u0648 \u0628\u0644\u0627\u0633\u0679\u0633 \u067e\u0631 \u06c1\u06cc\u0648\u0645\u0646 \u0679\u06cc\u0644\u0648\u0645\u0631\u06cc\u0632 \u0627\u06cc\u0645 \u0622\u0631 \u0627\u06cc\u0646 \u0627\u06d2 \u06a9\u06d2 \u0639\u0644\u0627\u062c \u06a9\u06d2 \u0627\u062b\u0631\u0627\u062a<\/li>\n<li>Atypical Hutchinson-Gilford Progeria Syndrome<\/li>\n<li>\u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u06a9\u06d2 \u0686\u0634\u0645\u06cc \u0645\u0638\u0627\u06c1\u0631<\/li>\n<li>\u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0645\u06cc\u06ba \u0645\u06cc\u0646\u0627\u0631\u0686<\/li>\n<li>\u06c1\u0686\u0646\u0633\u0646-\u06af\u0644\u0641\u0648\u0631\u0688 \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0633\u0646\u0688\u0631\u0648\u0645 \u0633\u06cc\u0644\u0632 \u0645\u06cc\u06ba \u0642\u0628\u0644 \u0627\u0632 \u0648\u0642\u062a \u0633\u0646\u0633\u0646\u06cc P53 \u0627\u06cc\u06a9\u0679\u06cc\u0648\u06cc\u0634\u0646 \u06a9\u06d2 \u0646\u062a\u06cc\u062c\u06d2 \u0645\u06cc\u06ba \u0646\u0642\u0644 \u06a9\u06d2 \u062f\u0628\u0627\u0624 \u06a9\u06d2 \u062c\u0648\u0627\u0628 \u0645\u06cc\u06ba<\/li>\n<li>\u0645\u0627\u0626\u06cc\u06a9\u0631\u0648 \u0622\u0631 \u0627\u06cc\u0646 \u0627\u06d2 29 \u06a9\u06cc \u0634\u0645\u0648\u0644\u06cc\u062a \u0686\u0648\u06c1\u0648\u06ba \u0645\u06cc\u06ba \u067e\u0631\u0648\u062c\u0631\u0627\u0626\u0688 \u0641\u06cc\u0646\u0648\u0679\u0627\u0626\u067e \u06a9\u0627 \u0628\u0627\u0639\u062b \u0628\u0646\u062a\u06cc \u06c1\u06d2\u06d4<\/li>\n<li>\u06a9\u0644\u0627\u0633\u06cc\u06a9\u06cc \u06c1\u0686\u0646\u0633\u0646-\u06af\u0644\u0641\u0648\u0631\u0688 \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0633\u0646\u0688\u0631\u0648\u0645 \u0648\u0627\u0644\u06d2 \u0628\u0686\u0648\u06ba \u06a9\u06d2 \u0627\u06cc\u06a9 \u0686\u06be\u0648\u0679\u06d2 \u06af\u0631\u0648\u067e \u0645\u06cc\u06ba \u0645\u062c\u0645\u0648\u0639\u06cc \u0627\u0648\u0631 \u0639\u0645\u062f\u06c1 \u0645\u0648\u0679\u0631 \u0646\u062a\u0627\u0626\u062c<\/li>\n<li>\u067e\u06cc\u062a\u06be\u0648\u0644\u0648\u062c\u06cc\u06a9\u0644 \u06c1\u0645\u0648\u0627\u0631 \u067e\u0679\u06be\u0648\u06ba \u06a9\u06d2 \u062e\u0644\u06cc\u0648\u06ba \u06a9\u06cc \u0639\u0645\u0631 \u0628\u0691\u06be\u0646\u06d2 \u06a9\u0648 \u062a\u06cc\u0632 \u06a9\u0631\u0646\u06d2 \u06a9\u06d2 \u0644\u0626\u06d2 \u0645\u0627\u0626\u06a9\u0631\u0648 \u067e\u06cc\u0679\u0631\u0646 \u0648\u0627\u0644\u06d2 \u0633\u0628\u0633\u0679\u0631\u06cc\u0679\u0633<\/li>\n<li>\u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0646 \u06a9\u06cc \u06a9\u0645 \u0633\u0637\u062d \u06a9\u0627 \u0646\u062a\u06cc\u062c\u06c1 \u0648\u0642\u062a \u06a9\u06d2 \u0633\u0627\u062a\u06be \u0627\u06cc\u0688\u06cc\u067e\u0648\u0632 \u0679\u0634\u0648 \u06a9\u06cc \u06a9\u0645\u06cc \u0645\u06cc\u06ba \u06c1\u0648\u062a\u0627 \u06c1\u06d2\u06d4<\/li>\n<li>Atypical Progeroid Syndrome Lamin A \u06a9\u06d2 \u06a9\u0648\u0627\u0626\u0644\u0688 \u06a9\u0648\u0627\u0626\u0644 \u0688\u0648\u0645\u06cc\u0646 \u0645\u06cc\u06ba \u062a\u0628\u062f\u06cc\u0644\u06cc \u06a9\u06cc \u0648\u062c\u06c1 \u0633\u06d2<\/li>\n<li>\u0633\u0644\u06cc\u06a9\u0679\u0688 \u0644\u0648\u0626\u0631 \u0627\u06cc\u06a9\u0633\u0679\u0631\u06cc\u0645\u0679\u06cc (LE) \u0631\u06cc\u0646\u062c \u0622\u0641 \u0645\u0648\u0634\u0646 (ROM) \u06a9\u0627 \u062a\u0639\u0644\u0642 \u06c1\u0686\u0646\u0633\u0646-\u06af\u0644\u0641\u0648\u0631\u0688 \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0633\u0646\u0688\u0631\u0648\u0645 \u0645\u06cc\u06ba \u062c\u0633\u0645\u0627\u0646\u06cc \u06a9\u0627\u0631\u06a9\u0631\u062f\u06af\u06cc \u0627\u0648\u0631 \u0639\u0645\u0631 \u0633\u06d2 \u062e\u0631\u0627\u0628\u06cc<\/li>\n<li>\u0644\u06cc\u0645\u0646\u0632 \u06a9\u06d2 \u0633\u0627\u062a\u06be \u0679\u06cc\u0644\u0648\u0645\u06cc\u0631\u06a9 \u067e\u0631\u0648\u0679\u06cc\u0646 AKTIP \u06a9\u0627 \u0641\u0646\u06a9\u0634\u0646\u0644 \u0627\u0648\u0631 \u0679\u0627\u067e\u0648\u0644\u0648\u062c\u06cc\u06a9\u0644 \u0627\u0646\u0679\u0631\u067e\u0644\u06d2\u06d4<\/li>\n<li>Hutchinson-Gilford Progeria Syndrome \u0645\u06cc\u06ba \u0628\u0642\u0627 \u067e\u0631 Farnesylation inhibitors \u06a9\u06d2 \u0627\u062b\u0631\u0627\u062a \u067e\u0631 \u0627\u067e \u0688\u06cc\u0679<\/li>\n<li>\u0646\u06cc\u0648\u06a9\u0644\u06cc\u0626\u0631 \u0644\u0641\u0627\u0641\u06c1 \u067e\u0631\u0648\u0679\u06cc\u0646 \u0644\u0648\u0645\u0627 \u0639\u0627\u0645 \u06a9\u0627\u0631\u0688\u06cc\u06a9 \u0641\u0646\u06a9\u0634\u0646 \u06a9\u06d2 \u0644\u06cc\u06d2 \u0642\u0627\u0628\u0644 \u0627\u0633\u062a\u0639\u0645\u0627\u0644 \u06c1\u06d2\u06d4<\/li>\n<li>\u0394133p53 Isoform \u06c1\u0686\u0646\u0633\u0646-\u06af\u0644\u0641\u0648\u0631\u0688 \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0633\u0646\u0688\u0631\u0648\u0645 \u06a9\u06d2 \u0644\u0626\u06d2 \u0627\u06cc\u06a9 \u0646\u0627\u0648\u0644 \u0639\u0644\u0627\u062c \u06a9\u06d2 \u06c1\u062f\u0641 \u06a9\u06d2 \u0637\u0648\u0631 \u067e\u0631<\/li>\n<li>\u067e\u0631\u06cc \u0644\u06cc\u0645\u06cc\u0646 \u0627\u06d2 \u0645\u06cc\u06ba ZMPSTE24 \u06a9\u0644\u06cc\u0648\u06cc\u062c \u0633\u0627\u0626\u0679 \u06a9\u0648 \u062e\u062a\u0645 \u06a9\u0631\u0646\u06d2 \u0648\u0627\u0644\u06cc \u062a\u0628\u062f\u06cc\u0644\u06cc \u067e\u0631\u0648\u062c\u0631\u0627\u0626\u0688 \u0688\u0633 \u0622\u0631\u0688\u0631 \u06a9\u0627 \u0633\u0628\u0628 \u0628\u0646\u062a\u06cc \u06c1\u06d2<\/li>\n<li>\u06a9\u0645 \u0646\u0645\u0628\u0631: \u0639\u0627\u0645 \u0639\u0645\u0631 \u0627\u0648\u0631 \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0645\u06cc\u06ba \u0639\u0627\u0645 \u0631\u0627\u0633\u062a\u06c1\u061f \u0627\u0646\u0633\u0627\u0646\u06cc \u062c\u0644\u062f \u06a9\u06d2 \u0645\u0627\u0626\u06a9\u0631\u0648 \u0628\u0627\u06cc\u0648\u0645 \u0645\u06cc\u06ba \u0627\u0645\u0648\u0646\u06cc\u0627 \u0622\u06a9\u0633\u06cc\u0688\u0627\u0626\u0632\u0646\u06af \u0628\u06cc\u06a9\u0679\u06cc\u0631\u06cc\u0627 \u0628\u0637\u0648\u0631 \u0633\u0648\u0632\u0634 \u0627\u06cc\u062c\u0646\u0679<\/li>\n<li>\u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0627\u0648\u0631 \u0688\u0631\u0645\u06cc\u0679\u0648\u0644\u0648\u062c\u06cc: \u0627\u06cc\u06a9 \u0628\u06be\u0648\u0644\u06cc \u06c1\u0648\u0626\u06cc \u06a9\u06c1\u0627\u0646\u06cc\u061f<\/li>\n<li>\u06c1\u0686\u0646\u0633\u0646-\u06af\u0644\u0641\u0648\u0631\u0688 \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0633\u0646\u0688\u0631\u0648\u0645 \u0679\u0631\u0627\u0646\u0633\u062c\u06cc\u0646\u06a9 \u0686\u0648\u06c1\u0648\u06ba \u0633\u06d2 \u0627\u0628\u062a\u062f\u0627\u0626\u06cc \u0628\u0639\u062f \u0627\u0632 \u067e\u06cc\u062f\u0627\u0626\u0634 \u06a9\u06cc\u0631\u0627\u0679\u06cc\u0646\u0648\u0633\u0627\u0626\u0679\u0633\u060c \u0627\u0648\u0633\u0679\u06cc\u0648 \u0628\u0644\u0648\u0633\u0679\u0633 \u0627\u0648\u0631 \u0627\u0648\u0633\u0679\u06cc\u0648 \u0633\u0627\u0626\u06cc\u0679\u0633 \u06a9\u0627 \u0679\u0631\u0627\u0646\u0633\u06a9\u0631\u067e\u0679 \u062a\u062c\u0632\u06cc\u06c1<\/li>\n<li>G608G \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0645\u0627\u0624\u0633 \u0645\u0627\u0688\u0644 \u067e\u0631 \u0639\u0644\u0627\u062c \u06a9\u06cc \u0633\u06a9\u06cc\u0644\u06cc\u0679\u0644 \u0627\u0641\u0627\u062f\u06cc\u062a \u06a9\u0627 \u0645\u0648\u0627\u0632\u0646\u06c1<\/li>\n<li>\u06c1\u0686\u0646\u0633\u0646-\u06af\u0644\u0641\u0648\u0631\u0688 \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0633\u0646\u0688\u0631\u0648\u0645 \u06a9\u06d2 \u062f\u0627\u0646\u062a\u0648\u06ba \u0627\u0648\u0631 \u06a9\u0631\u06cc\u0646\u06cc\u0648 \u0641\u06cc\u0634\u0644 \u0627\u0638\u06c1\u0627\u0631: \u0627\u06cc\u06a9 \u0637\u0648\u0644\u0627\u0646\u06cc \u0645\u0637\u0627\u0644\u0639\u06c1<\/li>\n<li>G608G \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0645\u0627\u0624\u0633 \u0645\u0627\u0688\u0644 \u0645\u06cc\u06ba \u06a9\u0627\u0631\u0679\u0644\u06cc\u062c \u06a9\u06cc \u0633\u0627\u062e\u062a\u06cc \u062e\u0635\u0648\u0635\u06cc\u0627\u062a \u0627\u0648\u0631 \u0628\u0627\u0626\u06cc\u0648 \u06a9\u06cc\u0645\u06cc\u06a9\u0644 \u06a9\u0645\u067e\u0648\u0632\u06cc\u0634\u0646 \u06a9\u06cc \u0646\u06af\u0631\u0627\u0646\u06cc \u06a9\u06d2 \u0644\u06cc\u06d2 \u06a9\u0646\u0679\u0631\u0627\u0633\u0679 \u0627\u06cc\u0646\u06c1\u0646\u0633\u0688 \u0645\u0627\u0626\u06cc\u06a9\u0631\u0648 \u0633\u06cc \u0679\u06cc (CEuCT)<\/li>\n<li>\u06c1\u0686\u0646\u0633\u0646 \u06af\u0644\u0641\u0648\u0631\u0688 \u067e\u0631\u0648\u062c\u06cc\u0631\u06cc\u0627 \u0633\u0646\u0688\u0631\u0648\u0645 \u067e\u0631 \u0645\u0646\u0634\u06cc\u0627\u062a \u06a9\u06cc \u062c\u0627\u0646\u0686<\/li>\n<\/ul>\n<p>\u062a\u06cc\u0633\u0631\u0627 \u062f\u0646 \u0633\u06cc\u0644 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src=\"https:\/\/www.progeriaresearch.org\/assets\/images\/medical_images\/Dr-Rothman-posing-question-(1).jpg\" alt=\"\" width=\"275\" height=\"204\" \/><p class=\"wp-caption-text\">\u0648\u0631\u06a9\u0634\u0627\u067e \u06a9\u06d2 \u0622\u0631\u06af\u0646\u0627\u0626\u0632\u0631 \u0688\u0627\u06a9\u0679\u0631 \u0641\u0631\u06cc\u0646\u06a9 \u0631\u0648\u062a\u06be\u0645\u06cc\u0646 \u0646\u06d2 \u0627\u06cc\u06a9 \u0633\u0648\u0627\u0644 \u0627\u0679\u06be\u0627\u06cc\u0627\u06d4<\/p><\/div>\n<p>\u06a9\u06cc\u062a\u06be\u0631\u06cc\u0646 \u0648\u0644\u0633\u0646\u060c \u067e\u06cc \u0627\u06cc\u0686 \u0688\u06cc (\u062c\u0627\u0646\u0632 \u06c1\u0627\u067e\u06a9\u0646\u0632 \u0633\u06a9\u0648\u0644 \u0622\u0641 \u0645\u06cc\u0688\u06cc\u0633\u0646\u060c \u06cc\u0648 \u0627\u06cc\u0633 \u0627\u06d2) \u0646\u06d2 \u0627\u067e\u0646\u0627 \u06a9\u0627\u0645 \u0627\u0646\u0632\u0627\u0626\u0645 \u0627\u0648 \u062c\u06cc \u0679\u06cc \u06a9\u0648 \u062f\u06cc\u06a9\u06be\u062a\u06d2 \u06c1\u0648\u0626\u06d2 \u067e\u06cc\u0634 \u06a9\u06cc\u0627 \u062c\u0648 \u067e\u0631\u0648\u0679\u06cc\u0646 \u06a9\u0648 \u0646\u0634\u0627\u0646\u06c1 \u0628\u0646\u0627\u0646\u06d2 \u06a9\u06d2 \u0644\u06cc\u06d2 \u0634\u0648\u06af\u0631 \u06a9\u06d2 \u0645\u0627\u0644\u06cc\u06a9\u06cc\u0648\u0644 \u06a9\u0648 \u062c\u0648\u0691\u062a\u0627 \u06c1\u06d2 \u0627\u0648\u0631 \u062a\u0645\u0627\u0645 \u062e\u0644\u06cc\u0648\u06ba \u06a9\u06d2 \u0644\u06cc\u06d2 \u0636\u0631\u0648\u0631\u06cc \u06c1\u06d2\u06d4 Giovanna Lattanzi\u060c PhD (CNR Institute for Molecular Genetics, Italy) \u0646\u06d2 \u0627\u067e\u0646\u06d2 \u0646\u062a\u0627\u0626\u062c \u067e\u06cc\u0634 \u06a9\u06cc\u06d2 \u06a9\u06c1 retinoic acid \u0627\u0648\u0631 rapamycin lamin A \u0633\u06d2 prelamin A \u06a9\u06d2 \u062a\u0646\u0627\u0633\u0628 \u0645\u06cc\u06ba \u0627\u0636\u0627\u0641\u06c1 \u06a9\u0631\u062a\u06d2 \u06c1\u06cc\u06ba \u0627\u0633 \u0637\u0631\u062d \u0633\u06cc\u0644 \u0645\u06cc\u06ba DNA \u0645\u0631\u0645\u062a \u06a9\u06cc \u0645\u0634\u06cc\u0646\u0631\u06cc \u06a9\u0648 \u0628\u0686\u0627\u062a\u06d2 \u06c1\u06cc\u06ba\u06d4 Gerardo Ferbeyre, MD, PhD (Universit\u00e9 de Montr\u00e9al, Canada) HGPS \u062e\u0644\u06cc\u0627\u062a \u0645\u06cc\u06ba endogenous mutant lamin A \u06a9\u06d2 \u0627\u0646\u0679\u0631\u0641\u06cc\u0633 \u0633\u06cc\u0631\u06cc\u0646 22 \u0641\u0627\u0633\u0641\u0648\u0631\u06cc\u0644\u06cc\u0634\u0646 \u06a9\u0627 \u0645\u0637\u0627\u0644\u0639\u06c1 \u06a9\u0631 \u0631\u06c1\u06d2 \u06c1\u06cc\u06ba \u062c\u0628\u06a9\u06c1 \u06a9\u0648\u0644\u0646 \u0633\u0679\u06cc\u0648\u0631\u0679\u060c \u0688\u06cc \u0641\u0644 (\u0627\u0646\u0633\u0679\u06cc \u0679\u06cc\u0648\u0679 \u0622\u0641 \u0645\u06cc\u0688\u06cc\u06a9\u0644 \u0628\u06cc\u0627\u0644\u0648\u062c\u06cc\u060c \u0633\u0646\u06af\u0627\u067e\u0648\u0631) \u0646\u06d2 SUN1 \u067e\u0631 \u062a\u0648\u062c\u06c1 \u0645\u0631\u06a9\u0648\u0632 \u06a9\u06cc \u06c1\u06d2\u060c 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\u0639\u0646\u0648\u0627\u0646 \u0627\u06cc\u0645\u0631\u062c\u0646\u06af \u062a\u06be\u06cc\u0631\u0627\u067e\u06cc\u0648\u0679\u06a9\u0633 \u062a\u06be\u0627\u060c \u0679\u0627\u0645 \u0645\u06cc\u0633\u0679\u06cc\u0644\u06cc\u060c \u067e\u06cc \u0627\u06cc\u0686 \u0688\u06cc (NIH\/\u0646\u06cc\u0634\u0646\u0644 \u06a9\u06cc\u0646\u0633\u0631 \u0627\u0646\u0633\u0679\u06cc \u0679\u06cc\u0648\u0679\u060c USA) \u06a9\u06d2 \u0633\u0627\u062a\u06be \u0634\u0631\u0648\u0639 \u06c1\u0648\u0627\u06d4 \u062c\u0646\u06c1\u0648\u06ba \u0646\u06d2 \u0645\u0645\u06a9\u0646\u06c1 \u0639\u0644\u0627\u062c \u06a9\u06d2 \u0644\u06cc\u06d2 \u0627\u0645\u06cc\u062f\u0648\u0627\u0631\u0648\u06ba \u06a9\u06cc \u062f\u0648\u0627\u0626\u06cc\u0648\u06ba \u06a9\u06cc \u062a\u0644\u0627\u0634 \u06a9\u0627 \u0627\u06cc\u06a9 \u062c\u0627\u0626\u0632\u06c1 \u067e\u06cc\u0634 \u06a9\u06cc\u0627\u06d4 \u0641\u0631\u0627\u0646\u0633\u0633 \u06a9\u0648\u0644\u0646\u0632\u060c \u0627\u06cc\u0645 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